February 26-28, 2017 • Atlanta, GA


  |  Auditory Neuropathy – Unique Children, Unique Outcomes

Auditory Neuropathy – Unique Children, Unique Outcomes

Auditory Neuropathy Spectrum disorder (ANSD) first published in 1996 by Starr et al. describes patients who have normal cochlear function present with abnormal neural function of the brainstem and/or VIIth nerve (Rance 2014). Twenty years later, more children are being identified with ANSD however there is still controversy with regards to management of these cases (Ching et al 2013). There are a variety of etiologies and outcomes surrounding ANSD, with each child requiring a unique management strategy to provide the best result for both the family and child. All families require extensive counseling, thus empowering them to become advocates for their child and their needs. This presentation will primarily focus on newborn screening leading to diagnosis with regards to different etiologies, monitoring and treatment plans including misdiagnosis with related case studies. Case examples will include unilateral ANSD, Cochlear Implants, Hearing aids, maturation, absent/hypoplastic nerves with a review of their language outcomes compared to their management strategies. Case studies represent an average age of diagnosis at 2.4 years + 2.6 years. Appropriate rehabilitation occurred at an average 3.6 years + 3.2 years. Over 50% of these case studies have a secondary medical disorder e.g. syndrome, developmental delay etc. This data shows a wide range of diagnosis and rehabilitation ages but overall delays from the standard 1, 3 and 6 month EDHI goals. We anticipate that this information will allow participants to review current local clinic practice to help this population be identified earlier and to meet EDHI goals, create a unique management plan with a family-centered approach and explore all treatment options with families to ensure the best suited is being chosen for the child and their family.

  • Participants to be able to review etiologies associated with ANSD and their implications
  • Participants to review different possible management strategies for different etiologies
  • Review current clinical protocols to create family centered approaches for this population

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Katie Sawaya (), Nemours, kathleen.sawaya@nemours.org;
Katie is a pediatric audiologist that has worked in New Zealand, England, Ireland and the United States over the past 10 years. She has worked with different newborn hearing screening programs and children's hospitals to help implement evidence based practice to help improve hearing services for children. She currently works for Nemours Specialty Clinic in Jacksonville, Florida. Her passion includes newborn hearing screening, electrophysiology, auditory neuropathy, hearing aid rehabilitation and cochlear implantation.


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